Acute abdominal - hyperlipidemia syndrome

[Outlined]
Acute abdominal - high fat blood syndrome (Acute Abdomen - Hyperlipemia Syndrome),
also known as familial high blood group type I lipoprotein, high chylous particulate
familial hyperlipidemia, familial hyperlipidemia primary, hepatosplenomegaly of lipid
deposition disease, hypercholesterolemia Huang lipomatosis, idiopathic of lipid deposition,
Hypercholesterolemia Huang lipomatosis, idiopathic lipid deposition disease and acute
abdomen - hyperlipidemia syndrome. In 1932, Burger and Grutz first two reports, it is also
called Burger-Grutz syndrome. For familial autosomal recessive genetic disease. Clinical
rare.
[Diagnosis]
According to clinical manifestations in after-induced fat intake on the abdominal
pain, pancreatitis, and other symptoms and signs such as skin of yellow light can be
carried out with hyperlipidemia diagnosis.
[Treatment]
The main treatment for the low-fat diet. Request control fat intake in calories only
the 20% to 25%. The medium chain fatty acid compounds alternative glycerol ordinary fat.
When suffering from acute pancreatitis for the corresponding treatment.
【Pathological changes:
Visibility on the pathology of the skin yellow, rich in reticular cells (such as bone
marrow, liver, spleen) Visibility foam cells, inflammation of the pancreas have
pathological changes.
Clinical manifestations】 【
Chang began in early childhood morbidity. Gender may be suffering from. When fat
intake can be induced, expressed as upper abdominal discomfort, anorexia, abdominal pain,
no more nausea and vomiting. Febrile seizures can be accompanied by abdominal pain,
abdominal tenderness, pancreatitis and peritoneal irritation sign, hepatosplenomegaly,
spleen area have no tenderness. About 30% of the patients in the health ministries
(including the mucosa) of visible yellow, or on the basis of erythema in a yellow nodules.
After the attack of yellow faded in the last few weeks, or even disappear altogether.
【Auxiliary inspection --
Patients with static at 4 ° C in the upper deck were white environment for the type I
Hyperlipoproteinemia. Lipoprotein analysis showed that: very low density lipoprotein
(VLDL), low-density lipoprotein (LDL), high-density lipoprotein (HDL) normal or reduced.
Increased cholesterol, triglyceride increase. When increased leukocyte attack, liver
function and normal glucose tolerance test.
【Prognosis:
The prognosis of the disease with other types of hyperlipidemia, the difficulty seems
to be complicated by atherosclerosis. Danger is recurrent pancreatitis.